Large And Medium Size Vessel And Single Organ Vasculitis 1st Ed 2021 Eds Carlo Salvarani by (eds) Carlo Salvarani, Luigi Boiardi, Francesco Muratore 9783030671747, 9783030671778, 9783030671754, 3030671747, 3030671771, 3030671755 instant download after payment.

The vasculitides are a heterogeneous group of relatively rare conditions that can
occur independently by other conditions (primary vasculitis), or they can represent
a manifestation of a well-established disease (secondary vasculitis). Vasculitis may
be localized to a single organ or vascular bed, or, they are, more commonly, generalized.
The most widely accepted classification system, the 2012 Revised Chapel Hill
Consensus Conference (2012 CHCC), is based on vessel size predominantly
involved (large-, medium-, and small-vessel vasculitis) and association with antineutrophil
cytoplasmic antibodies (ANCA). (Jennette JC, Falk RJ, Bacon PA, et al.
2012 revised International Chapel Hill Consensus Conference Nomenclature of
Vasculitides. Arthritis Rheum. 2013;65(1):1–11). Furthermore, vasculitis affecting
vessels of variable size and single organ vasculitis are included. According to the
2012 CHCC definition, single organ vasculitis is a vasculitis involving arteries or
veins of any size in a single organ without evidences indicating the presence of a
systemic vasculitis. The involved organ and vessel type should be included in the
name (e.g., cutaneous small-vessel vasculitis, testicular arteritis, central nervous
system vasculitis). Vasculitis distribution may be unifocal or multifocal (diffuse)
within an organ.
This book will provide detailed and updated information on the nosology, pathology,
pathogenesis, clinical presentation, diagnosis, and treatment of large- and
medium-sized vessel and single organ vasculitis, critically discussed by the most
expert physicians and researchers in the field. Among the conditions considered are
giant cell arteritis, Takayasu arteritis, polyarteritis nodosa, primary central nervous
system vasculitis, isolated aortitis, isolated gastrointestinal vasculitis, cutaneous
vasculitis, and isolated genitourinary vasculitis. Finally, arterial and venous involvement
in Behcet’s disease will be discussed as well.